Subacute Sclerosing Panencephalitis with Subclinical Infection:

V. A. Kotrashetti; Vijay Baburao Sonawane; Kapil Bainade; Shweta Nair; Amit Vatkar; Santosh Kumar

doi:10.21276/aanat.2020.6.2.2

V. A. Kotrashetti Professor, DY Patil Hospital, Vidyanagar, Sector 5, Nerul, Navi Mumbai, Maharashtra, India
Vijay Baburao Sonawane Associate Professor, DY Patil Hospital, Vidyanagar, Sector 5, Navi Mumbai, Maharashtra, India
Kapil Bainade Assistant Professor, DY Patil Hospital, Vidyanagar, Sector 5, Nerul, Navi Mumbai, Maharashtra, India
Shweta Nair Senior Resident, DY Patil Hospital, Vidyanagar, Sector 5, Nerul, Navi Mumbai, Maharashtra, India
Amit Vatkar Assistant Professor, DY Patil Hospital, Vidyanagar, Sector 5, Nerul, Navi Mumbai, Maharashtra, India
Santosh Kumar Junior Resident, DY Patil Hospital, Vidyanagar, Sector 5, Nerul, Navi Mumbai, Maharashtra, India

DOI: https://doi.org/10.21276/aanat.2020.6.2.2

Keywords: Subacute Sclerosing Panencephalitis, Neurodegenerative, Myoclonic Jerks

Abstract

Subacute Sclerosing Panencephalitis (SSPE) is a chronic complication of measles. It is a neurodegenerative disorder characterized by cognitive and memory deterioration, behaviour abnormalities, involuntary movements and repetitive myoclonic jerks and a steady motor decline. We report a case of a 7-year-old girl with subacute sclerosing panencephalitis presenting with myoclonic jerks, regression of motor milestones and speech. The child was not immunised for measles. Magnetic resonance imaging revealed multiple variable-sized ill-defined T2W and FLAIR hyperintense areas are seen involving the white matter of the bilateral fronto-parietal lobes. Electroencephalograph findings and CSF analysis confirmed the diagnosis of subacute sclerosing panencephalitis.

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